Prevalence, clinical profile, and prognosis of NPM mutations in AML with normal karyotype.

نویسندگان

  • Nicolas Boissel
  • Aline Renneville
  • Valeria Biggio
  • Nathalie Philippe
  • Xavier Thomas
  • Jean-Michel Cayuela
  • Christine Terre
  • Isabelle Tigaud
  • Sylvie Castaigne
  • Emmanuel Raffoux
  • Stephane De Botton
  • Pierre Fenaux
  • Herve Dombret
  • Claude Preudhomme
چکیده

Mutation of the nucleophosmin (NPM) gene has been reported as the most frequent mutation in acute myeloid leukemia (AML), especially in the presence of a normal karyotype. In this subgroup of intermediate-risk AML, the identification of other gene mutations (eg, FLT3, CCAAT/enhancer-binding protein-alpha [CEBPA]) has helped to refine the prognosis. This study explored the prevalence and the prognostic impact of NPM mutations in a cohort of 106 patients with normal-karyotype AML. NPM exon 12 mutations were detected by polymerase chain reaction (PCR) and fragment analysis for the insertion/deletion globally resulting in a 4-bp insertion. NPM mutations were detected in 47% of patients and were associated with a high white blood cell count, involvement of the monocytic lineage (M4/M5), and a decreased prevalence of CEBPA mutations. Complete remission rate and long-term outcome did not differ between NPM-mutated and -nonmutated patients. Prospective studies are needed to confirm the definitive place of NPM mutation detection to predict AML response to therapy.

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عنوان ژورنال:
  • Blood

دوره 106 10  شماره 

صفحات  -

تاریخ انتشار 2005